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第十章 结缔组织病
Connective Tissue Diseases
系统性红斑狼疮 Systemic Lupus Erythematosus,SLE
是侵犯皮肤和全身多脏器的一种自身免疫性疾病。
诊断要点:
多见于中青年女性。面部有蝶形红斑,手、足可有充血或出血斑,常伴雷诺征。患者光敏感,有肌肉、关节症状。可侵犯肾脏、心脏、肺脏和中枢神经系统,严重者威胁生命。实验室检查抗核抗体、Sm抗体等阳性。血白细胞总数低,尿中可有蛋白。
治疗要点:
应卧床休息,避免日光照晒。系统用糖皮质激素和/或免疫抑制剂,全身对症、支持治疗。
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-1_13914.jpg?sign=1739585803-XZeSkQNdfmpm2qeWySofDd60I55CITKu-0-1abc935fbf43e703658eeeaf4e8e1285)
图10-1-1 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-2_13912.jpg?sign=1739585803-3zQs53wojgsRJP21YrqqnMe9ueLGQ61l-0-51c1489be4238ea4cc7f40186633136f)
图10-1-2 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-3_13916.jpg?sign=1739585803-VgouLuppHEpJbmBqzPUpfpnSrT7QWO5G-0-ab07a79b429b3d8afc3e0e7c5bef4059)
图10-1-3 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-4_13915.jpg?sign=1739585803-i6ASH08QLVB3DHkKWYmf7Hamjml0sRNu-0-2a1402502880654bf03c9f611f2926df)
图10-1-4 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-5_13913.jpg?sign=1739585803-SLBAWBC2tN1BzRdeGvGbxmLkiUKpcZNy-0-8288329678dc6e0511e4a69bdde8c2b6)
图10-1-5 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-6_13918.jpg?sign=1739585803-8mt8ED69jeckMQKin6zqxVN8lJCNDk2x-0-49b18094329f705e8a4c970e85eafd6a)
图10-1-6 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-7_13919.jpg?sign=1739585803-SDpjUIJ2wHL5ENa5ENgT9MTZUJu4L3nJ-0-53f95d291ef490fc97a251c66b143913)
图10-1-7 系统性红斑狼疮